No | Ventilatory supportat referral | Age atreferral | Age at onset of maskventilation (years) | Current age(years) |
1 | NPV | 4 years | 8 | 21 |
2 | PPV via tracheostomy | 4 weeks | 9 | 19 |
3 | PPV via tracheostomy | 4 weeks | 11 | 19 |
4 | NPV | 12 weeks | 3 | 18 |
5 | PPV via ETT | 2 years | 9 | 15 |
6 | PPV via ETT | 4 weeks | 2 | 14 |
7 | None | 10 weeks | 9 | 14 |
8 | PPV via tracheostomy | 14 months | 3 | 13 |
9 | PPV via ETT | 8 weeks | 1.5 | 11 |
ETT, endo tracheal tube; NPV, negative pressure ventilation; PPV, positive pressure ventilation.