Feature | Frequency (%) |
Macroglossia | 93 |
Pre or postnatal growth >90th centile | 88 |
Abdominal wall defects | 80 |
Ear creases or pits | 76 |
Facial naevus flammeus | 62 |
Renal abnormalities | 59 |
Hypoglycaemia | 50 |
Hemihypertrophy | 24 |
Cardiac malformation | 7 |
Intestinal malrotation | 5 |
Neoplasia | 4 |
Mental retardation | 4 |