Case No | Grade of enceph | Neonatal MRI | Tests of visual function at school age | Neuro exam | Cognitive level | ||||||
---|---|---|---|---|---|---|---|---|---|---|---|
Pattern of lesion | OR | PVC | Age at test | Orthop | Crowding acuity | Stereo | Fields | ||||
Abn, abnormal; Athet CP, athetoid cerebral palsy; BG, basal ganglia; Bil, bilateral; Dys, dystonic; enceph, encephalopathy; m, months; Min, Minimal; Mod, moderate; MR, mental retardation; MRI, magnetic resonance imaging; Neuro, neurological; OR, optic radiations; Orthop, orthopsis; PVC, primary visual cortex; Sev, severe; Stereo, stereopsis; Tetra, tetraplegia; Untest, untestable; WM, white matter; y, years. | |||||||||||
*Unable to fix and follow; –, not tested. | |||||||||||
1 | 1 | Normal | N | N | 5y 9m | N | N | N | N | N | N |
2 | 1 | Normal | N | N | 5y 10m | N | N | N | N | N | N |
3 | 1 | Normal | N | N | 6y 0m | N | N | N | N | N | N |
4 | 1 | Normal | N | N | 6y 5m | N | N | N | N | N | N |
5 | 1 | Normal | N | N | 5y 11m | N | N | N | N | N | N |
6 | 2 | Normal | N | N | 5y 10m | N | N | N | N | N | N |
7 | 1 | Normal | N | N | 6y 2m | N | N | N | N | N | N |
8 | 2 | Normal | N | N | 5y 7m | N | Abn | N | N | N | N |
9 | 1 | Min WM | N | N | 6y 0m | N | N | N | Bil narrow | N | N |
10 | 1 | Min WM | N | N | 5y 11m | Squint | N | N | N | N | N |
11 | 1 | Min WM | N | N | 5y 7m | N | N | N | N | N | N |
12 | 1 | Min WM | N | N | 5y 6m | N | N | N | N | N | N |
13 | 2 | Min WM | N | N | 6y 6m | N | N | N | N | N | N |
14 | 1 | Min WM | N | N | 5y 5m | N | Abn | N | N | N | N |
15 | 1 | Min WM | N | N | 5y 7m | N | N | N | N | N | N |
16 | 2 | Min WM | N | N | 5y 5m | N | N | N | N | N | N |
17 | 2 | Min WM | N | N | 5y 7m | N | N | N | N | N | N |
18 | 2 | Mod WM | N | N | 6y 6m | N | N | N | N | N | N |
19 | 2 | Mod WM | N | N | 5y 6m | N | N | N | N | N | N |
20 | 2 | Mod WM | N | N | 5y 7m | N | N | N | N | N | N |
21 | 2 | Mod WM (haem) | N | N | 5y 10m | N | N | N | N | N | N |
22 | 2 | Mod WM (haem) | N | N | 5y 6m | N | N | N | N | N | N |
23 | 2 | Sev WM | Abn | Abn | 5y 8m | Squint | Abn | Abn | Bil narrow | Diplegia | Sev MR |
24 | 2 | Sev WM | Abn | Abn | 5y 8m | Squint | Abn | Abn | Bil narrow | Diplegia | Mod MR |
25 | 2 | Sev WM | N | Abn | 5y 11m | Abn* | Untest | Untest | Untest | Diplegia | Mod MR |
26 | 2 | Min BG | N | N | 5y 6m | N | N | N | N | N | N |
27 | 2 | Min BG | N | N | 5y 5m | N | N | N | N | Athet CP | N |
28 | 1 | Min BG | N | N | 5y 2m | N | N | N | N | N | N |
29 | 2 | Mod BG | N | N | 5y 6m | N | N | N | N | N | N |
30 | 2 | Mod BG | N | N | 5y 6m | N | Abn | Abn | N | Dys Tetra | Mod MR |
31 | 2 | Mod BG, sev WM | Abn | Abn | 5y 10m | Squint | Abn | Abn | Bil narrow | Tetra | Mod MR |
32 | 2 | Mod BG, sev WM | Abn | Abn | 5y 9m | N | Abn | – | Bil narrow | Tetra | Mod MR |
33 | 2 | Mod BG, sev WM | Abn | Abn | 5y 6m | Squint | Abn | Abn | Bil narrow | Tetra | Mod MR |
34 | 2 | Sev BG & WM | Abn | Abn | 5y 10m | Abn* | Untest | Untest | Untest | Tetra | Sev MR |
35 | 2 | Sev BG & WM | Abn | Abn | 6y 0m | Abn* | Untest | Untest | Untest | Tetra | Sev MR |
36 | 3 | Sev BG & WM | Abn | Abn | 5y 5m | Abn* | Untest | Untest | Untest | Tetra | Sev MR |
37 | 2 | Sev BG & WM | N | N | 5y 6m | Abn* | Untest | Untest | Untest | Tetra | Sev MR |
38 | 2 | Sev BG & WM | Abn | Abn | 5y 5m | Abn* | Untest | Untest | Untest | Tetra | Sev MR |
39 | 2 | Sev BG & WM | Abn | Abn | 5y 9m | Abn* | Untest | Untest | Untest | Tetra | Sev MR |