PT  - JOURNAL ARTICLE
AU  - Suresh Chandran
AU  - Meng Keang Lim
AU  - Victor Yu-Hei Yu
TI  - Fetal acalvaria with amniotic band syndrome
AID  - 10.1136/fn.82.1.F11
DP  - 2000 Jan 01
TA  - Archives of Disease in Childhood - Fetal and Neonatal Edition
PG  - F11--F13
VI  - 82
IP  - 1
4099  - http://fn.bmj.com/content/82/1/F11.short
4100  - http://fn.bmj.com/content/82/1/F11.full
SO  - Arch Dis Child Fetal Neonatal Ed2000 Jan 01; 82
AB  - A case of amniotic band syndrome (ABS) presenting with acalvaria is reported. ABS includes a spectrum of non-genetic anomalies, varying from simple digital band constriction to major craniofacial and visceral defects, and even fetal death. Acalvaria is a rare congenital malformation characterised by the absence of the dome-like superior portion of the cranium comprising the frontal, parietal, and occipital bones and dura mater, in the presence of a normal skull base and facial bones with complete cranial contents. No two cases are the same. Acrania or absence of the flat skull bones with disorganised cerebral hemispheres have been reported in the presence of amniotic bands. ABS is an aetiological factor in acalvaria. Appropriate counselling for affected families needs to be given after prenatal diagnosis.